In people with maple syrup urine disease, the body is unable to metabolize the amino acids leucine, isoleucine, and valine. One of the symptoms is that the ...What Are the Signs & Symptoms of Maple Syrup Urine Disease? Newborns with MSUD have pee or earwax that smells sweet, like maple syrup. They also may: have problems with feeding; vomit; be fussy or irritable; have a high-pitched cry; have a low energy level and be very sleepy; A baby or child with MSUD also might have: trouble growing and ...Various Causes: The maple syrup smell in dogs can be due to dietary factors, yeast infections, bacterial infections, or medical conditions like canine diabetes or maple syrup urine disease. Importance of Observation: Paying attention to changes in your dog’s breath smells, fur scent, and overall health is crucial. A sudden sweet smell ...Urine that smells sweet or like maple syrup; Lack of coordination or weakness; Seizures; What Should I Do If I Am Concerned? Call Mass General at 617-726-2000. Ask the operator to page the Genetics and Metabolism doctor on call; Bring your child to the emergency room (ED). Have the doctors follow the steps below. What the ED Should KnowNewborns with MSUD have pee or earwax that smells sweet, like maple syrup. They also may: have problems with feeding. vomit. be fussy or irritable. have a high-pitched cry. …Robert Burakoff, MD. Like urine color, the smell of your urine can be a clue about your body's condition. Smelly urine can also be caused by factors such as: Certain foods. Dehydration. Diabetes ...Amino acids. Seizures Maple syrup urine disease (MSUD) is a metabolism disorder passed down through families in which the body cannot break down certain parts of proteins. Urine in persons with this condition can smell like maple syrup. Causes. Maple syrup urine disease (MSUD) is caused by a gene defect.The seeds are used in cooking, to make medicine, or to hide the taste of other medicine. Fenugreek seeds smell and taste somewhat like maple syrup. Fenugreek leaves are eaten in India as a vegetable. How fenugreek causes maple syrup smell or body odor. Fenugreek is taken by mouth for digestive problems such as loss of appetite, …Maple syrup urine disease is an inherited disorder in which the body is unable to process certain protein building blocks (amino acids) properly. The condition gets its name from the distinctive sweet odor of affected infants' urine. It is also characterized by poor feeding, vomiting, lack of energy (lethargy), abnormal movements, and delayed ...Urine is made up mostly of water. But it also has waste in it that comes from the kidneys. What is in the waste and how much there is causes urine odor. Urine with a lot of water and little waste has little to no odor. If urine has a lot of waste with little water, also called concentrated, it might have a strong odor from a gas called ammonia.Oct 7, 2016 · Symptoms of the disease range depending on the type. Some of the initial symptoms of classic MSUD include irregular sleep patterns, lethargy, irritability, weight loss, poor appetite, and a distinctive maple sugar odor in earwax, sweat, and urine (which gives the disorder its name). If untreated, MSUD can lead to significant physical and ... Jun 28, 2021 · A musty or sweet odor may also indicate mold growth. But overall, most molds produce a sweet and earthy smell. Mold growth is particularly common in basements due to unnoticed water leaks and moisture seepage on walls. Insect infestation can also cause your house to smell like maple syrup. Thus, if you notice the smell, it’s best to look ... Another agreed, but thought it more like “[f]ruity, floral, socks.” Of course, there was the boring assessor who was like, uh, smells like fenugreek. This is a harmless phenomenon; the only reason I bring it up is that there is actually a serious congenital disorder called maple syrup urine disease: branched-chain ketoaciduria.3. Yeast Infection. Sometimes, the maple syrup smells from the dog’s fur rather than its urine or breath. In cases like these, yeast infestation is the most likely cause. The area around the pup’s ears and nose are the most common places where yeast infections occur as they trap moisture, encouraging yeast growth.Maple Syrup Urine Disease – MSUD. Maple Syrup Urine Disease is an inherited disorder in which the body is unable to process certain protein building blocks (amino acids) properly. The condition gets its name from the distinctive sweet odor of affected infants’ urine. It is also characterized by poor feeding, vomiting, lack of energy ...Around the same time, I experienced a similar thing, albeit not in New York. There would be a strong smell of maple syrup around the block I lived on for seemingly no reason. We had maple trees, but by that point we had been living there for several years before I smelled anything like that, and by the 2010s I stopped smelling it entirely.Like sugary cereal I was thinking fruit loops. I can smell it all the time I don’t have to put my face on her diaper to smell it! She is 2 months and EBF. I googled it today and the first thing that came up was maple syrup urine disease and now I’m so freaked out bc it seems super serious!!!1. **Dietary Factors:** One of the most common reasons why a cat may smell like maple syrup is their diet. Certain ingredients in cat food, such as corn or wheat, can produce a sweet smell reminiscent of maple syrup when metabolized by the body. 2. **Diabetes:** Another possible explanation for a cat smelling like maple syrup is diabetes.Some medical conditions (or eating fenugreek in high quantities) can cause urine/sweat to smell like syrup. Pour some water down the drain, make sure it's not a gas coming up. I'd air out the room too, and see if you can't literally pinpoint the smell by finding where in the room it smells like it's coming from. Reply reply.Aug 24, 2012 · aripatsim Discussion starter. 159 posts · Joined 2012. #1 · Aug 24, 2012. Last night while holding my rats and giving them so kisses I noticed they smelled a bit like maple syrup and their cage has a very faint smell of syrup, too. I did a google search of this and found a little bit of information, but not really what I was looking for. Aug 15, 2011 · Strange smells. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the body's inability to digest certain amino acids MONTREAL, May 06, 2021 (GLOBE NEWSWIRE) -- Rogers Sugar Inc.’s (“our,” “we”, “us” or “Rogers”) (TSX: RSI) today reported second quarter fiscal 2... MONTREAL, May 06, 2021 (GLOBE ...Various Causes: The maple syrup smell in dogs can be due to dietary factors, yeast infections, bacterial infections, or medical conditions like canine diabetes or maple syrup urine disease. Importance of Observation: Paying attention to changes in your dog’s breath smells, fur scent, and overall health is crucial. A sudden sweet smell ...The 5 Reasons Your Dog Smells Like Maple Syrup. 1. Diet. Some foods or treats that contain maple syrup, molasses, or other sweet ingredients can make your dog’s breath smell like maple syrup. If ...aripatsim Discussion starter. 159 posts · Joined 2012. #1 · Aug 24, 2012. Last night while holding my rats and giving them so kisses I noticed they smelled a bit like maple syrup and their cage has a very faint smell of syrup, too. I did a google search of this and found a little bit of information, but not really what I was looking for.This causes symptoms such as: Pee or earwax that smells like maple syrup. Lethargy and ill temper. Feeding problems and poor appetite. Seizures or abnormal movements. …If your urine smells like sugar or has a sweet smell, it might mean diabetes. 10-06-2004 03:46 PM by incorporeal. R Kelly could help you out. FTW.May 2, 2021 · It is also the number one reason for the sweet scent of maple syrup in dogs. At its core, “diabetes” means high blood sugar, a condition caused by an insufficient amount of insulin in the body to counteract it. This high concentration of blood sugar is why a dog’s breath or urine (and sometimes his coat) may smell like maple syrup. While ... Sweet smelling urine may be due to an underlying condition, such as diabetes, dehydration, a yeast infection, or a genetic condition called maple syrup urine disease. Urine can reveal a lot about ...urine that smells like maple syrup or burnt sugar; Babies with MSUD have episodes of illness called metabolic crisis This is a serious health condition caused by low blood sugar and the build-up of toxic substances in the blood. Symptoms of a metabolic crisis are poor appetite, nausea, vomiting, diarrhea, extreme sleepiness, irritable mood and ... A build-up of these amino acids (especially leucine) disturbs brain cells and results in brain swelling and problems with brain cell growth, leading to physical and intellectual disability and, if untreated, death. The classic form of MSUD usually presents with irritability, extreme sleepiness, and lack of feeding within the first few days of life. If your cat smells like maple syrup, it may be a medical reason. A rare urine disease usually causes the smell in cats called feline hyperesthesia syndrome or FHS. In general, dogs and cats have odorless urine, but any kind of stress—emotional or physical—can cause their bodies to produce sugars and proteins in their urine.What Are the Signs & Symptoms of Maple Syrup Urine Disease? Newborns with MSUD have pee or earwax that smells sweet, like maple syrup. They also may: have problems with feeding; vomit; be fussy or irritable; have a high-pitched cry; have a low energy level and be very sleepy; A baby or child with MSUD also might have: trouble growing and ...Maple syrup urine disease (MSUD) is a rare inherited condition that causes the urine to have a maple syrup smell. It occurs due to a lack of an enzyme activity that breaks down certain amino acids. Without treatment, it can lead to potentially life threatening complications. Learn about the types, symptoms, causes, and more of MSUD.Taking a lot of vitamin C? It could tweak your pee’s odor. Pregnancy, too, can bring about hormonal changes that affect how your pee smells. 4. Rare Conditions: MSUD and More. Rare metabolic disorders like Maple Syrup Urine Disease (MSUD) can give your pee a distinct sweet scent due to amino acid buildup. Table 1: Potential Causes and ...A musty or sweet odor may also indicate mold growth. But overall, most molds produce a sweet and earthy smell. Mold growth is particularly common in basements due to unnoticed water leaks and moisture seepage on walls. Insect infestation can also cause your house to smell like maple syrup. Thus, if you notice the smell, it’s best to look ... Answer: Causes of Sweet Smell in urine. There are various causes of sweet smell in the urine. Most are transient and due to metabolizing various foods. Sometimes strong odor is due to highly concentrated urine when one hasn't consumed enough water, easily fixed. An unusual body and urine odor has been reported after drinking fenugreek tea. This doesn't seem to be harmful, but it could be confused with a condition called "maple syrup urine disease."The only specific finding that is unique to MSUD is the development of a characteristic odor, reminiscent of maple syrup that can most readily be detected in the urine and earwax and may be smelled within a day or two of birth.MSUD stands for “maple syrup urine disease.”. It is named for the sweet maple syrup smell of the urine in untreated babies. This condition is one type of amino acid disorder. People with MSUD have problems breaking down certain amino acids found in protein. Maple Syrup Urine Disease (MSUD) | USMLE Step 1 Biochemistry Mnemonic.The 5 Reasons Your Dog Smells Like Maple Syrup. 1. Diet. Some foods or treats that contain maple syrup, molasses, or other sweet ingredients can make your dog’s breath smell like maple syrup. If ...Discover the pros and cons of maple, oak, cherry, and birch cabinets. Learn which wood is best for your kitchen remodel. Get expert advice and tips now. Expert Advice On Improving ...A musty or sweet odor may also indicate mold growth. But overall, most molds produce a sweet and earthy smell. Mold growth is particularly common in basements due to unnoticed water leaks and moisture seepage on walls. Insect infestation can also cause your house to smell like maple syrup. Thus, if you notice the smell, it’s best to look ...Reasons why men excrete bad-smelling urine are bladder infection, liver problems, dehydration, diabetes and urinary tract infections, as well as maple syrup urine disease, gastroin...Nov 23, 2015 · Oldest First. s. sunbaby13. Nov 22, 2015 at 7:08 PM. There is something called maple syrup disease but this is usually ruled out in newborn screens and you would have already had problems within the first few months of life, so probably not that! I would talk to her pediatrician if you are concerned. Oldest First. s. sunbaby13. Nov 22, 2015 at 7:08 PM. There is something called maple syrup disease but this is usually ruled out in newborn screens and you would have already had problems within the first few months of life, so probably not that! I would talk to her pediatrician if you are concerned.Classic maple syrup urine disease (MSUD) is typically diagnosed in newborns, whereas nonclassic forms may manifest at any age. We describe a 58-year-old man presenting with recurrent encephalopathy, found with a nonclassic form of MSUD. This patient case highlights the importance of considering inborn errors of metabolism in the …Urine that smells like maple syrup. Vomiting. Exams and Tests. These tests may be done to check for this disorder: Plasma amino acid test. Urine organic acid …MONTREAL, May 06, 2021 (GLOBE NEWSWIRE) -- Rogers Sugar Inc.’s (“our,” “we”, “us” or “Rogers”) (TSX: RSI) today reported second quarter fiscal 2... MONTREAL, May 06, 2021 (GLOBE ...The urine odor in this condition smells like maple syrup, which is why it is called maple syrup urine disease (MSUD), also called BCKDC disease, branched-chain ketoacid dehydrogenase deficiency, or branched-chain ketonuria-1. ... breathing difficulties, and sweet maple syrup odor in urine, start to appear. If left unmanaged, an affected …Overview. Causes. Warning signs. When to see a doctor. Outlook. Urine may smell sweet if it contains extra glucose, a type of sugar. Sweet smelling urine may be due to an underlying...The National Institutes of Health (NIH) describes maple syrup urine disease as "a rare but serious inherited condition" that renders the body unable to process some amino acids from protein-rich ...Twenty minutes later, she hopped off of her machine, but the smell remained. I sniffed. It was me. I was the one that smelled. I reeked of waffles. On the subway ride home, with confusion growing ...INTRODUCTION. Maple syrup urine disease (MSUD), also known as branched-chain ketoaciduria (BCKA), is a clinically rare autosomal-recessive disorder of branched-chain amino acid (BCAA) metabolism that is caused by deficiency of the branched-chain α-ketoacid dehydrogenase (BCKD) complex[].MSUD was first reported …Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. It is caused by a defect in 1 of 3 genes. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. This leads to a buildup of these chemicals in the blood. In the most severe form, MSUD can damage the brain during ...A build-up of these amino acids (especially leucine) disturbs brain cells and results in brain swelling and problems with brain cell growth, leading to physical and intellectual disability and, if untreated, death. The classic form of MSUD usually presents with irritability, extreme sleepiness, and lack of feeding within the first few days of life.Nov 23, 2015 · Oldest First. s. sunbaby13. Nov 22, 2015 at 7:08 PM. There is something called maple syrup disease but this is usually ruled out in newborn screens and you would have already had problems within the first few months of life, so probably not that! I would talk to her pediatrician if you are concerned. May 28, 2021 · “Maple syrup urine disease (MSUD) is a rare but serious inherited condition. It means the body cannot process certain amino acids (the “building blocks” of protein), causing a harmful build-up of substances in the blood and urine.” Summary If your dog’s urine smells like maple syrup then it is most likely due to canine diabetes. Some medical conditions (or eating fenugreek in high quantities) can cause urine/sweat to smell like syrup. Pour some water down the drain, make sure it's not a gas coming up. I'd air out the room too, and see if you can't literally pinpoint the smell by finding where in the room it smells like it's coming from. Reply reply.Hubby and I have lived in our 100-year old farmhouse for about 2 years now. One of the upstairs bedrooms, as well as the attic, have a puzzling smell which I can't figure out what might be the cause. The odor is very sweet, like maple syrup; it's always faintly noticeable, worse if the room door is kept closed for a while.If you are dehydrated, your urine may smell like ammonia. Maple syrup urine disease. This genetic disease can cause the amino acids leucine, isoleucine and valine to build up in the blood. People with this condition may have urine that smells like maple syrup. Type 2 diabetes. Uncontrolled high blood sugar can cause urine to smell …aripatsim Discussion starter. 159 posts · Joined 2012. #1 · Aug 24, 2012. Last night while holding my rats and giving them so kisses I noticed they smelled a bit like maple syrup and their cage has a very faint smell of syrup, too. I did a google search of this and found a little bit of information, but not really what I was looking for.There's a disease in humans called maple syrup urine disease caused by a defect in a metabolic enzyme required to break down branched chain amino acids... Could possibly occur in a cat? Not a vet so I don't know, but it's very rare in humans so just a thought to consider in case your vet doesn't identify the problem right away. A build-up of these amino acids (especially leucine) disturbs brain cells and results in brain swelling and problems with brain cell growth, leading to physical and intellectual disability and, if untreated, death. The classic form of MSUD usually presents with irritability, extreme sleepiness, and lack of feeding within the first few days of life. Classic Severe Maple Syrup Urine Disease (Classic Severe MSUD; MSUD Type IA): Characterized by a progressive infantile cerebral dysfunction defined as lethargy, failure to thrive and weight loss, severe metabolic derangement, hypotonia and/or hypertonia, progressive encephalopathy, seizures, and rapidly coma. Affected newborns …Maple Syrup Urine Disease (MSUD) is an inherited disorder so named because one of its first signs is urine that has an odor reminiscent of maple syrup. The underlying defect disrupts the metabolism of certain amino acids. These are amino acids that have a branched side chain. Because they cannot be fully broken down, they accumulate in the …Started taking fenugreek the other day since I noticed my supply was decreasing and now my pee smells like maple syrup. I knew this might happen but I hoped I'd avoid it. It's kind of gross. Archived post. New comments cannot be posted and votes cannot be cast. My ear wax smells like maple syrup. My husband calls it my "spicy ear wax".Meth is a highly addictive stimulant drug that is synthesized into a crystalline form. The resulting crystals can then be smoked, crushed, and snorted; dissolved and injected; or even swallowed. Meth produces a fast, euphoric high, but it can also cause devastating damage to the brain and body.Maple syrup urine disease is a rare inherited disorder caused by the body’s inability to properly process amino acids, leading to a characteristic odor of maple syrup in the …Possible side effects and cautions: Sweat and urine smells like maple syrup; milk and/or breastfed baby may smell like maple syrup. Reply ... On an unrelated note, apparently theres a genetic disorder that makes it so your pee smells like maple syrup. ReplyMy first thought is that your boyfriend might have maple syrup urine disease (unrelated to diabetes) or diabetic ketoacidosis, which is serious diabetes complication where the body produces excess ...Cat Pee Smells Like Maple Syrup - Vet Explains Pets. If you’ve ever noticed that your cat’s pee smells like maple syrup, you’re not alone. This unusual …Feb 28, 2024 ... ... and urine the way they do in the breath of DKA patients, causing the urine to smell like maple syrup. That smell used to be what led to ...Nov 29, 2023 · The herb fenugreek, often taken to boost breastmilk production, can make urine smell like maple syrup. Yeast infections can give your urine an unusual odor as well. Often described as yeasty, it can sometimes make urine smell sweet. A musty or sweet odor may also indicate mold growth. But overall, most molds produce a sweet and earthy smell. Mold growth is particularly common in basements due to unnoticed water leaks and moisture seepage on walls. Insect infestation can also cause your house to smell like maple syrup. Thus, if you notice the smell, it’s best to …Fluffy pancakes are a breakfast staple that never fails to delight. There’s something truly satisfying about biting into a stack of light and airy pancakes, topped with butter and ...Oct 11, 2016 · a distinctive maple sugar odor in earwax, sweat, and urine. irregular sleep patterns. alternating episodes of hypertonia (muscle rigidity) and hypotonia (muscle limpness) high-pitched cry. Signs ... Like sugary cereal I was thinking fruit loops. I can smell it all the time I don’t have to put my face on her diaper to smell it! She is 2 months and EBF. I googled it today and the first thing that came up was maple syrup urine disease and now I’m so freaked out bc it seems super serious!!!Posted 09-03-10. I noticed tonight that my son's fleece pajamas smelled like maple syrup. For the past two or three days his pajamas have that smell. His urine does not smell like maple syrup, but ...A build-up of these amino acids (especially leucine) disturbs brain cells and results in brain swelling and problems with brain cell growth, leading to physical and intellectual disability and, if untreated, death. The classic form of MSUD usually presents with irritability, extreme sleepiness, and lack of feeding within the first few days of life.Twenty minutes later, she hopped off of her machine, but the smell remained. I sniffed. It was me. I was the one that smelled. I reeked of waffles. On the subway ride home, with confusion growing ...Japanese maples grow slowly, but they are beautiful and colorful in the fall. Learn how to care for them in this article. Advertisement The Japanese maple (Acer palmatum) is a deci...Maple syrup urine disease is a rare and incurable genetic disease that causes urine to smell like maple syrup. People with the disease can’t break down the amino acids leucine, isoleucine, and ...C.L. answers from Chicago on April 19, 2008. Please take your baby in to a pediatrician. There is metabolic condition which causes urine to smell like maple syrup. It is usually picked up on the metabolic screen the state does on newborns. But, your baby may have been missed. Early treatment is vital.Takeaway. A possible cause of “sweet-smelling” stool is an Clostridioides difficile infection, which has several symptoms including diarrhea. “Sweet smelling” is not often a description ...
Amino acids. Seizures Maple syrup urine disease (MSUD) is a metabolism disorder passed down through families in which the body cannot break down certain parts of proteins. Urine in persons with this condition can smell like maple syrup. Causes. Maple syrup urine disease (MSUD) is caused by a gene defect.. Skeleton ar 15 parts
Mar 11, 2011 ... About a year ago I noticed the same thing with my daughter and was concerned because there is a condition called Maple Syrup Urine Disease. The ...Maple Syrup Urine Disease (MSUD) Maple Syrup Urine Disease, although rare, is a serious condition that can cause your cat to emit a syrup-like smell. This condition is related to a deficiency in enzymes needed to break down certain amino acids like phenylalanine. If not treated, it can lead to severe health issues for your cat.What the Smell of Your Poop Can Tell You About Your Gut Health. 7. If Your Urine Smells Like Coffee... We'll keep this short and sweet: "Some people notice that they have a coffee smell to their urine after drinking coffee," Dr. Agarwal says. Fix it: This is harmless — keep on caffeinating.It is also the number one reason for the sweet scent of maple syrup in dogs. At its core, “diabetes” means high blood sugar, a condition caused by an insufficient amount of insulin in the body to counteract it. This high concentration of blood sugar is why a dog’s breath or urine (and sometimes his coat) may smell like maple syrup. While ...Started taking fenugreek the other day since I noticed my supply was decreasing and now my pee smells like maple syrup. I knew this might happen but I hoped I'd avoid it. It's kind of gross. Archived post. New comments cannot be posted and votes cannot be cast. My ear wax smells like maple syrup. My husband calls it my "spicy ear wax".One such condition is maple syrup urine disease, which gets its name from the fact that (as you may have guessed) the urine of affected infants smells distinctly like maple syrup. It’s uncommon, but can be serious if left untreated. “For the most part,” says Dr. Diamond, “the occasional unpleasant smell is just a dirty diaper and no ...When temperatures in the southern megacity of Shenzhen hover around 90 degrees this time of year, people head to outdoor swimming pools in droves. But they might want to consider a...Likewise, certain foods could be the reason your urine smells like popcorn. In particular, ground fenugreek seeds give off an aroma similar to maple syrup or butterscotch, and that can change the ...Maple syrup is a beloved natural sweetener that adds a unique flavor to a variety of dishes. While maple syrup is produced in several regions across North America, Vermont stands o...A musty or sweet odor may also indicate mold growth. But overall, most molds produce a sweet and earthy smell. Mold growth is particularly common in basements due to unnoticed water leaks and moisture seepage on walls. Insect infestation can also cause your house to smell like maple syrup. Thus, if you notice the smell, it’s best to look ...Maple syrup urine disease (MSUD) type 1B is an inherited metabolic disorder named for the characteristic maple syrup smell of the affected person’s urine. If carefully treated with a low-protein diet, people with MSUD can live fairly normal lives. What is maple syrup disease? Maple syrup urine disease (MSUD) is a rare metabolic disorder that ...Vermont is renowned for its breathtaking landscapes, charming towns, and rich traditions. One tradition that stands out is the production of maple syrup. The state boasts a long hi...Urine, sweat, and even the earwax of people with MSUD will often have a sweet smell similar to maple syrup or burnt sugar. The severity and number of symptoms varies for each person with the...Mar 11, 2021 · Like sugary cereal I was thinking fruit loops. I can smell it all the time I don’t have to put my face on her diaper to smell it! She is 2 months and EBF. I googled it today and the first thing that came up was maple syrup urine disease and now I’m so freaked out bc it seems super serious!!! Some medical conditions (or eating fenugreek in high quantities) can cause urine/sweat to smell like syrup. Pour some water down the drain, make sure it's not a gas coming up. I'd air out the room too, and see if you can't literally pinpoint the smell by finding where in the room it smells like it's coming from. Reply reply.These amino acids need to be oxidized, but without the proper enzyme, they accumulate in the blood. They eventually spill over into the urine, giving it a maple syrup-like smell. So, before you start worrying about your blood sugar, rest assured that your odor is MOST LIKELY caused by your protein intake.The researchers noted that signs of both maple syrup urine disease and alkaptonuria — also called black urine disease — could be spotted in earwax before blood and urine tests found them. “Odors in earwax may be able to tell us what a person has eaten and where they have been,” Dr. George Preti, an organic chemist at Monell, said …Maple syrup urine disease (MSUD) is a condition in which the body is unable to break down certain proteins. The condition is named for the sweet odor of the urine of untreated babies. MSUD is considered an amino acid condition because people with MSUD have trouble breaking down certain amino acids, the building blocks of proteins..